Table 2 |
|
|
A list of major IgG4-related disease in various organs. |
|
|
Organ |
Manifestation |
|
|
|
|
Pituitary gland |
Hypophysitis |
|
Meningis |
Pachymeningitis |
|
Lacrimal gland |
Chronic sclerosing dacryoadenitis (Mikulicz's disease) |
|
Salivary gland |
Chronic sclerosing sialadenitis (Küttner's tumour) |
|
Lymph node |
Lymphadenopathy with 5 histological subtypes |
|
- Multicentric Castleman disease-like (type I) |
|
|
- Follicular hyperplasia (type II) |
|
|
- Interfollicular expansion (type III) |
|
|
- Progressive transformation of germinal centre (type IV) |
|
|
- Nodal inflammatory pseudotumor (type V) |
|
|
Thyroid |
Thyroiditis or hypothyroidism |
|
Skin |
Pseudolymphoma |
|
Breast |
Inflammatory pseudotumour or mastitis |
|
Lung |
Inflammatory pseudotumour |
|
Focal or diffuse interstitial pneumonia |
|
|
Inflammation in bronchovascular bundles. |
|
|
Pleura |
Nodular pleuritis |
|
Stomach |
Chronic gastritis or ulcer |
|
Vater's ampulla |
Pseudotumourous enlargement |
|
Pancreas |
Type 1 autoimmune pancreatitis |
|
Bile duct |
Sclerosing cholangitis |
|
Gallbladder |
Lymphoplasmacytic sclerosing cholecystitis |
|
Liver |
Inflammatory pseudotumour |
|
Chronic active hepatitis (autoimmune hepatitis) |
|
|
Retroperitoneum |
Retroperitoneal fibrosis |
|
Aorta/artery |
Periaortitis/periarteritis |
|
Inflammatory aneurysm |
|
|
Kidney |
Tubulointerstitial nephritis |
|
Peripheral nerve |
Perineural mass |
|
|
|
|
Zen et al. Orphanet Journal of Rare Diseases 2011 6:82 doi:10.1186/1750-1172-6-82 |
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