Table 1

Comparison of type 1 and type 2 autoimmune pancreatitis (AIP).

Type 1AIP

Type 2 AIP


Age

Adult

Child and adult

Gender

Predominantly male

Almost equal

Serum IgG4 levels

Elevated

Normal

Histology

Histological nomenclature

Lymphoplasmacytic sclerosing pancreatitis (LPSP)

Idiopathic duct-centric pancreatitis

IgG4+ plasma cells

Many

Rare

Granulocytic epithelial lesion

Absent

Present

Relapse rate

High

Low

Extra-pancreatic lesions

IgG4-related disease as shown in Table 2

Inflammatory bowel disease


Zen et al. Orphanet Journal of Rare Diseases 2011 6:82   doi:10.1186/1750-1172-6-82

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