Table 1

Primary diagnostic criteria

Main features

Prominent/predominant distal sensory loss
Repeated foot ulcerations/acromutilations
Osteonecrosis

Additional criteria

Variable distal motor involvement
Foot deformity
Autonomic disturbances
Skin changes (hyperkeratosis, blisters, onychomycosis, etc.)
Autosomal dominant inheritance

Auer-Grumbach Orphanet Journal of Rare Diseases 2008 3:7   doi:10.1186/1750-1172-3-7