Table 2

Parietal pleural plaques, diffuse pleural thickening and lung fibrosis in the patients with retroperitoneal fibrosis (RPF) and the asbestos-exposed controls.

Radiological finding
RPF without asbestos exposure
RPF with asbestos exposure
Controls with ≥ 10 fy of asbestos exposure





N = 16
% (N)
<10 fy
N = 13
% (N)
≥ 10 fy
N = 9
% (N)
N = 18
% (N)

Pleural plaques




     class 0
68.8 (11)
23.1 (3)
11.1 (1)
22.2 (4)
     class 1
19.8 (3)
15.4 (2)
22.2 (2)
27.8 (5)
     class 2
12.5 (2)
38.5 (5)
33.3 (3)
27.8 (5)
     class 3–5
0 (0)
23.1 (3)
33.3 (3)
22.2 (4)
DPT




     class 0
75.0 (12)
46.2 (6)
44.4 (4)
61.1 (11)
     class 1
6.3 (1)
0 (0)
11.1 (1)
11.1 (2)
     class 2
18.8 (3)
23.1 (3)
0 (0)
33.3 (3)
     class 3
0 (0)
30.8 (4)
44.4 (4)
22.2 (2)
Lung fibrosis




     class 0
87.5 (14)
69.2 (9)
66.7 (6)
77.8 (14)
     class 1
12.5 (2)
15.4 (2)
22.2 (2)
11.1 (2)
     class 2
0 (0)
7.7 (1)
0 (0)
0 (0)
     class 3–5
0 (0)
7.7 (1)
11.1 (1)
11.1 (2)

(fy = fiber years, DPT = diffuse pleural thickening)

Uibu et al. Orphanet Journal of Rare Diseases 2008 3:29   doi:10.1186/1750-1172-3-29