Figure 4.

In longstanding forms, bony deformation affects the spine, with upper dorsal kyphosis and compensatory lumbar hyperlordosis. The thorax is deformed due to protuberance of the lower portion of the sternum, and by elongation and divergence of the ribs.

Chanson and Salenave Orphanet Journal of Rare Diseases 2008 3:17   doi:10.1186/1750-1172-3-17
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