Table 1

Diseases or disorders associated with PBC

Sjögren's syndrome (Sicca syndrome)

Scleroderma

Raynaud's disease

CREST syndrome


Calcinosis cutis

Raynaud's phenomenon

Esophageal dysmotility

Sclerodactyly

Telangiectases
Systemic lupus erythematosus

Rheumatoid arthritis

Mixed connective tissue disease

Polymyositis

Cutaneous disorders


Dermatomyositis

Lichen planus

Pemphigoid

Psoriasis
Autoimmune thrombocytopenic purpura

Pernicious anemia

Sarcoidosis

Myasthenia gravis

Autoimmune thyroid disease


Chronic thyroiditis (Hashimoto's disease)

Grave's disease (Basedow's disease)
Diabetes Type 1 (Insulin-dependent diabetes mellitus)

Addison's disease

Inflammatory bowel diseases


Celiac disease

Ulcerative colitis

Crohn's disease
Gallstones

Pulmonary fibrosis

Glomerulonephritis


Kumagi and Heathcote Orphanet Journal of Rare Diseases 2008 3:1   doi:10.1186/1750-1172-3-1