Table 3

Syndromic HPE with normal karyotype

Syndromic HPE with normal karyotype

214800
CHARGE syndrome gene CHD7 8q12
146510
Pallister Hall gene GLI3 7p13
270400
Smith Lemli Opitz DHCR7 11q12-q13
180849
Rubinstein-Taybi gene CREBBP 16p11.3
249000
Meckel syndrome
264480
Pseudotrisomy 13
192430
Velo cardio facial Synd gene TBX1 22q11.2
300073
HPE and fetal akynesia, X linked?
300571
HPE, ectrodactyly, cleft lip/palate, X linked?
300373
Osteopathia striata with cranial sclerosis Xp11.4-p11.22
245552
Lambotte syndrome
184705
Steinfeld Syndrome
601357
HPE, amelia, facial cleft
600674
Microtia-anotia
236680
Hydrolethalus syndrome
206900
Microphtalmia syndromic
156810
MLRD association
202650
Dysgnathia complex
601370
Genoa Syndrome

Dubourg et al. Orphanet Journal of Rare Diseases 2007 2:8   doi:10.1186/1750-1172-2-8