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Anatomical types of biliary atresia (BA) |
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| French classification |
Frequency |
Description |
Upper level of obstruction of the extrahepatic bile ducts |
US/UK/Japanese classification |
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|
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| Type 1 |
~3% |
Atresia limited to the common bile duct |
Common bile duct |
Type 1 |
| Type 2 |
~6% |
Cyst in the liver hilum communicating with dystrophic intrahepatic bile ducts |
Hepatic duct |
Type 2 |
| Type 3 |
19% |
Gallbladder, cystic duct and common bile duct patent |
Porta hepatis |
Type 3 |
| Type 4 |
72% |
Complete extrahepatic BA |
Porta hepatis |
Type 3 |
Chardot Orphanet Journal of Rare Diseases 2006 1:28 doi:10.1186/1750-1172-1-28 |
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